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Survivor of Rare Rapid-ageing Disease Progeria Dies at 28

Progeria, also known as Hutchinson–Gilford syndrome (HGPS), causes people to age rapidly, leading them to appear older than they are - (Photo by AFP)
Progeria, also known as Hutchinson–Gilford syndrome (HGPS), causes people to age rapidly, leading them to appear older than they are - (Photo by AFP)
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Survivor of Rare Rapid-ageing Disease Progeria Dies at 28

Progeria, also known as Hutchinson–Gilford syndrome (HGPS), causes people to age rapidly, leading them to appear older than they are - (Photo by AFP)
Progeria, also known as Hutchinson–Gilford syndrome (HGPS), causes people to age rapidly, leading them to appear older than they are - (Photo by AFP)

Sammy Basso, who was the longest living survivor of the rare genetic disease progeria, has died at the age of 28, the Italian Progeria Association said on Sunday.

Progeria, also known as Hutchinson–Gilford syndrome (HGPS), causes people to age rapidly, leading them to appear older than they are, with a reduced quality of life and a life expectancy of only 13.5 years without treatment, the association's website said.

It affects one in every eight million people born, and has a worldwide incidence of one in every 20 million, Reuters reported.

Born in 1995 in Schio, in the northern Italian region of Veneto, Basso was diagnosed with progeria at the age of two. In 2005, he and his parents founded the Italian Progeria Association.

He became famous through the National Geographic documentary "Sammy's Journey," which recounts his journey along Route 66 in the United States, from Chicago to Los Angeles, with his parents and one of his best friends, Riccardo.

"Today our light, our guide, has gone out. Thank you Sammy for making us part of this wonderful life," the association wrote on its Instagram page.

There are only 130 recognised cases of classic progeria worldwide, of which four are in Italy.

However, the Italian Progeria Association estimated there could be as many as 350 cases as they can be difficult to trace especially in developing countries.

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Russian ‘Spy Whale’ in Norway Wasn’t Shot Dead, Likely Died of Infection

FILE - In this photo taken in April 2019 a beluga whale found in Arctic Norway is fed. (Jorgen Ree Wiig, Norwegian Directorate of Fisheries via AP)
FILE - In this photo taken in April 2019 a beluga whale found in Arctic Norway is fed. (Jorgen Ree Wiig, Norwegian Directorate of Fisheries via AP)
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Russian ‘Spy Whale’ in Norway Wasn’t Shot Dead, Likely Died of Infection

FILE - In this photo taken in April 2019 a beluga whale found in Arctic Norway is fed. (Jorgen Ree Wiig, Norwegian Directorate of Fisheries via AP)
FILE - In this photo taken in April 2019 a beluga whale found in Arctic Norway is fed. (Jorgen Ree Wiig, Norwegian Directorate of Fisheries via AP)

A beluga whale that lived off Norway’s coast and whose harness ignited speculation that it was a Russian spy, was not shot to death as claimed by animal rights groups but died of a bacterial infection, Norwegian police said Friday.
A final autopsy by Norway's Veterinary Institute “concludes that the probable cause of death was bacterial infection -- possibly as a result of a wound in the mouth from a stuck stick,” Amund Preede Revheim, head of the North Sea and Environment section of the police in south-western Norway said.
“There have been no findings from the autopsy that indicate that the whale has been shot,” he stressed, adding that the autopsy had been “made difficult by the fact that many of the whale’s organs were very rotten.” As there was no indication of foul play, there was no reason to start a criminal investigation into its death, The Associated Press quoted Preede Revheim as saying.
The tame beluga, which was first spotted in 2019 not far from Russian waters with a harness reading “Equipment St. Petersburg,” had been nicknamed "Hvaldimir,” combining the Norwegian word for whale — hval — and the first name of Russian President Vladimir Putin.
It was found floating in a southern Norway bay on Aug. 31.
In September, animal advocate groups OneWhale and NOAH filed a police report saying that the animal’s wounds suggested it was intentionally killed.
They pointed at several wounds found on the animal’s skin, including what was interpreted as a bullet hole.
“Assessments made by the Veterinary Institute and the police’s forensic technicians are that these are not gunshot wounds. X-rays of the chest and head were carried out without any projectiles or other metal fragments being detected,” police said in a statement.
Earlier, police had described a stick about 35 centimeters (14 inches) long and 3 centimeters (1 inch) wide which was found wedged in the animal’s mouth, its stomach was empty and its organs had broken down, police said. No further details were given.
The 4.2-meter (14-foot) long and 1,225-kilogram (2,700-pound) whale was first spotted by fishermen not far from the Arctic town of Hammerfest.
Its harness, along with what appeared to be a mount for a small camera, led to media speculation that it was a “spy whale.” Experts say the Russian navy is known to have trained whales for military purposes. Media reports also have speculated that the whale might have been trained as a therapy animal.
There was no immediate reaction from OneWhale or NOAH.